ABP Pediatric Nephrology Practice Questions - ABP Pediatric Nephrology Subspecialty Certifying Examination Exam

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A 3-month-old presents with polyuria, polydipsia, dehydration, and serum Na 160 mEq/L. Despite DDAVP administration, urine osmolality remains 100 mOsm/kg. Which diagnosis is most likely?
Correct Answer:
Nephrogenic diabetes insipidus

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